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MS
unreviewed

Hypoxanthine-guanine phosphoribosyltransferase (HGPRT)

2 reactions · 1 pathways

Cofactors used

Clinical / pharmacological. Lesch-Nyhan syndrome: hyperuricaemia, self-mutilation, choreoathetosis, intellectual disability

What it does, reaction by reaction

2 reactions

Purine Salvage Pathway Nucleotide Metabolism · Cytosol

step 1 Irreversible

Hypoxanthine → IMP

Converts Hypoxanthine into IMP

Notes

HGPRT catalyzes hypoxanthine + PRPP → IMP + PPi. Mg2+ supports phosphoribosyl transfer, and PPi hydrolysis drives the reaction forward. This is effectively irreversible in vivo and salvages hypoxanthine directly to the central purine intermediate.

step 2 Irreversible

Guanine → GMP

Converts Guanine into GMP

Notes

HGPRT catalyzes guanine + PRPP → GMP + PPi. This is also effectively irreversible in vivo; the same enzyme therefore salvages both hypoxanthine and guanine.

Showing all 2 reactions.

What accelerates and inhibits it

Regulation is pathway-specific, so each context is listed separately

0 entries

No regulation recorded for this enzyme in the source documents.

Recent literature

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