What it does, reaction by reaction
Pyrimidine Degradation Nucleotide Metabolism · Cytosol
N-Carbamyl-beta-alanine → beta-alanine
Converts N-Carbamyl-beta-alanine into beta-Alanine
› Notes
Beta-ureidopropionase catalyzes N-carbamyl-beta-alanine + H2O → beta-alanine + NH3 + CO2. This completes the uracil-derived ring-carbon/nitrogen disposal sequence.
N-Carbamyl-beta-aminoisobutyrate → beta-aminoisobutyrate
Converts N-Carbamyl-beta-aminoisobutyrate into beta-Aminoisobutyrate
› Notes
Beta-ureidopropionase catalyzes N-carbamyl-beta-aminoisobutyrate + H2O → beta-aminoisobutyrate + NH3 + CO2.
Showing all 2 reactions.
What accelerates and inhibits it
Regulation is pathway-specific, so each context is listed separately
Pyrimidine Degradation
N-carbamyl-beta-amino acid availability
Product effects; inherited loss of function
No established direct hormonal control.
Recent literature
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