AGL AR unreviewed
Cori-Forbes disease (GSD III)
Enzyme or protein defect
Glycogen debranching enzyme
Accumulates or becomes deficient
Limit dextrin
Key features
Milder than GSD I; normal lactate, hepatomegaly, myopathy
Management
High-protein diet, frequent feeds
Not clinical guidance. Written from standard clinical biochemistry, not from the uploaded documents, and marked unreviewed. Teaching-level reference for study and database seeding only. It must not be used to manage a patient.
Recent literature
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