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MS
GALT AR unreviewed

Classic galactosaemia

Enzyme or protein defect

Galactose-1-phosphate uridylyltransferase

Accumulates or becomes deficient

Galactose-1-phosphate, galactitol

Key features

Cataracts, jaundice, hepatomegaly, intellectual disability, E. coli sepsis

Management

Exclude galactose and lactose

Not clinical guidance. Written from standard clinical biochemistry, not from the uploaded documents, and marked unreviewed. Teaching-level reference for study and database seeding only. It must not be used to manage a patient.

Recent literature

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