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MS
unreviewed

Glucocerebrosidase (GBA)

1 reactions · 1 pathways

Clinical / pharmacological. Gaucher disease; GBA variants also raise Parkinson disease risk

What it does, reaction by reaction

1 reactions

Sphingolipid Degradation (Lysosomal) Lipid Metabolism · Lysosome

step 4 Irreversible/directional

Glucosylceramide -> ceramide + glucose

Converts Glucosylceramide into Ceramide Glucose

Notes

Deficiency causes Gaucher disease, the commonest lysosomal storage disorder (Gaucher cells, bone crises, pancytopenia).

Showing all 1 reactions.

What accelerates and inhibits it

Regulation is pathway-specific, so each context is listed separately

0 entries

No regulation recorded for this enzyme in the source documents.

Recent literature

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