Skip to content
MS
MMUT / MMAA / MMAB AR unreviewed

Methylmalonic acidaemia

Enzyme or protein defect

Methylmalonyl-CoA mutase (or cobalamin handling)

Accumulates or becomes deficient

Methylmalonic acid

Key features

Ketoacidosis, hyperammonaemia, failure to thrive

Management

B12 (hydroxocobalamin) trial, protein restriction, carnitine

Not clinical guidance. Written from standard clinical biochemistry, not from the uploaded documents, and marked unreviewed. Teaching-level reference for study and database seeding only. It must not be used to manage a patient.

Recent literature

Nothing is fetched until you ask, so the page stays fast and the request is yours rather than automatic.

Europe PMC · ten most recent, newest first